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CIM11 LD2D.4

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-11

Gorlin syndrome

chapitre
20 Developmental anomalies
bloc
Multiple developmental anomalies or syndromes
definition
Gorlin syndrome, also known as naevoid basal cell carcinoma syndrome (NBCCS), is a hereditary condition characterised by a wide range of developmental abnormalities (odontogenic keratocysts of the jaws, hyperkeratosis of palms and soles, skeletal abnormalities, intracranial ectopic calcifications, a
inclusions
Naevoid basal cell carcinoma syndrome
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1012745138 ↗