CIM11 LD2D.0
CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-11
Peutz-Jeghers syndrome
- chapitre
- 20 Developmental anomalies
- bloc
- Multiple developmental anomalies or syndromes
- definition
- Peutz-Jeghers syndrome (PJS) is an autosomal dominant inherited disorder characterised by intestinal hamartomatous polyps in association with a distinct pattern of skin and mucosal macular melanin deposition. Patients have an increased risk of developing intestinal cancer.
- type
- category
- navigateur oms (fr)
- https://icd.who.int/browse/2026-01/mms/fr#969253189 ↗