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CIM11 LD24.03

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-11

Diastrophic dysplasia

chapitre
20 Developmental anomalies
bloc
Multiple developmental anomalies or syndromes
definition
Diastrophic dwarfism is a rare autosomal recessive disorder marked by short stature with short extremities (final adult height is 120cm +/- 10cm), and joint malformations leading to multiple joint contractures (principally involving the shoulders, elbows, interphalangeal joints and hips)
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1681550532 ↗