CIM11 LB16.1

Hirschsprung disease

chapitre: 20 Developmental anomalies
bloc: Structural developmental anomalies of the digestive tract
definition: This is a developmental anomaly affecting the intestinal tract characterised by congenital absence of myenteric ganglion cells (aganglionosis) in a segment of the large bowel. Due to the absence of intrinsic innervation of the muscle layers of the affected segment, there is a loss of motor function.
type: category
navigateur oms (fr): https://icd.who.int/browse/2026-01/mms/fr#1772690306 ↗