CIM11 8C76
CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09
Myofibrillar myopathy
- chapitre
- 08 Diseases of the nervous system
- bloc
- Primary disorders of muscles
- definition
- Myofibrillar myopathies are a heterogeneous group of disorders, characterised by the pathologic finding of myofibrillar disruption on electron microscope with a spectrum of histological abnormalities including excessive desmin accumulation in muscle fibres.
- exclusions
- Myasthenia gravis or certain specified neuromuscular junction disorders | Secondary myopathies
- type
- category
- navigateur oms (fr)
- https://icd.who.int/browse/2026-01/mms/fr#125656853 ↗