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CIM11 8A44.0

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Pelizaeus-Merzbacher disease

chapitre
08 Diseases of the nervous system
bloc
Multiple sclerosis or other white matter disorders
definition
Pelizaeus-Merzbacher disease (PMD) is an X-linked leukodystrophy characterised by developmental delay, nystagmus, hypotonia, spasticity, and variable intellectual deficit. It is classified into three sub-forms based on the age of onset and severity: connatal, transitional, and classic PMD.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1313582105 ↗