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CIM11 5C64.00

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Wilson disease

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Disorders of metabolite absorption or transport
definition
Wilson disease is an autosomal recessive disorder of copper metabolism characterised by the toxic accumulation of copper, mainly in the liver and central nervous system that may present as hepatic, neurologic or psychiatric forms.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#468161208 ↗