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CIM11 5C61.2

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Congenital sucrase-isomaltase deficiency

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Disorders of metabolite absorption or transport
definition
Congenital sucrase-isomaltase deficiency (CSID) is a carbohydrate intolerance disorder characterised by malabsorption of oligosaccharides and disaccharides. CSID is transmitted as an autosomal recessive trait and is caused by mutations in the brush-border membrane complex sucrase-isomaltase (SI), wh
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1817406536 ↗