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CIM11 5C58.12

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Erythropoietic porphyrias

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Erythropoietic porphyrias are associated clinically with photosensitivity and biochemically with abnormal accumulation of porphyrins in erythrocytes. They include erythropoietic protoporphyria and the very rare congenital erythropoietic porphyria.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1074667008 ↗