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CIM11 5C58.02

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Dubin-Johnson syndrome

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterised clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1691610999 ↗