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CIM11 5C57.0

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Disorders of peroxisome biogenesis

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Peroxisome biogenesis disorders (PBDs) include the Zellweger syndrome spectrum (PBD-ZSD) and rhizomelic chondrodysplasia punctata type 1 (RCDP1). PBD-ZSD represents a continuum of disorders including infantile Refsum disease, neonatal adrenoleukodystrophy, and Zellweger syndrome. Collectively, PBDs
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1919322367 ↗