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CIM11 5C56.32

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Mucopolysaccharidosis type 4

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Mucopolysaccharidosis type IV (MPS IV) is a lysosomal storage disease belonging to the group of mucopolysaccharidoses, and characterised by spondylo-epiphyso-metaphyseal dysplasia. It exists in two clinically indistinguishable forms, A and B. A deficiency in one of the two enzymes required for the d
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#2078241550 ↗