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CIM11 5C56.31

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Mucopolysaccharidosis type 2

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Mucopolysaccharidosis type 2 (MPS 2) is a lysosomal storage disease belonging to the group of mucopolysaccharidoses. The clinical picture ranges from severe (the most frequent form) with early psychomotor regression, facial dysmorphism (macroglossia, constantly opened mouth, coarse features), hepato
inclusions
Hunter syndrome
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1056274204 ↗