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CIM11 5C56.02

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Metachromatic leukodystrophy

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Metachromatic leukodystrophy is a neurodegenerative disease characterised by an accumulation of sulfatides (sulphated glycosphingolipids, especially sulfogalactosylceramides or sulfogalactocerebrosides) in the nervous system and kidneys. Three forms of the disease exist: late infantile, juvenile and
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#172326564 ↗