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CIM11 5C51.40

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Galactose-1-phosphate uridyltransferase deficiency

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Classic galactosemia is a life-threatening metabolic disease with onset in the neonatal period. Infants usually develop feeding difficulties, lethargy, and severe liver disease.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#2011000259 ↗