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CIM11 5C50.F0

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Prolidase deficiency

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Prolidase deficiency is a very rare inborn error of metabolism characterised by mild to severe skin lesions particularly on the face, palms, lower legs and soles, together with other variable features.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1416203271 ↗