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CIM11 5C50.A2

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Argininaemia

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Arginase deficiency is a rare autosomal recessive amino acid metabolism disorder characterised clinically by variable degrees of hyperammonemia, developing from about 3 years of age, and leading to progressive loss of developmental milestones and spasticity in the absence of treatment.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1619102598 ↗