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CIM11 5C50.12

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Tyrosinaemia type 2

chapitre
05 Endocrine, nutritional or metabolic diseases
bloc
Inborn errors of metabolism
definition
Tyrosinemia type 2 is an inborn error of tyrosine metabolism characterised by hypertyrosinemia with oculocutaneous manifestations (eye redness, photophobia, excessive tearing and pain, palmoplantar hyperkeratosis) and, in some cases, intellectual deficit.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#1900229795 ↗