CIM11 3A21.0
CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09
Paroxysmal nocturnal haemoglobinuria
- chapitre
- 03 Diseases of the blood or blood-forming organs
- bloc
- Acquired haemolytic anaemia
- definition
- Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired clonal hematopoietic stem cell disorder characterised by corpuscular haemolytic anaemia, bone marrow failure and frequent thrombotic events.
- exclusions
- Aplastic anaemia with paroxysmal nocturnal haemoglobulinuria | haemoglobinuria NOS
- type
- category
- navigateur oms (fr)
- https://icd.who.int/browse/2026-01/mms/fr#859588467 ↗