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CIM11 2A51

CIM-11 MMS (diagnostics, nouvelle classification OMS) — fichier du 2026-09-09

Myeloid neoplasm associated with PDGFRB rearrangement

chapitre
02 Neoplasms
bloc
Myeloid or lymphoid neoplasms with eosinophilia and abnormalities of PDGFRA, PDGFRB or FGFR1
definition
A distinct type of myeloid neoplasm that occurs in association with rearrangement of PDGFRB gene at 5q32. Patients usually present with a picture resembling chronic myelomonocytic leukaemia and, less often, atypical chronic myeloid leukaemia or chronic eosinophilic leukaemia.
type
category
navigateur oms (fr)
https://icd.who.int/browse/2026-01/mms/fr#625932159 ↗