| CIM11 |
4A01.00 |
Hereditary agammaglobulinaemia with profoundly reduced or absent B cells
|
|
| CIM11 |
4A01.01 |
Immunodeficiencies with severe reduction in at least two serum immunoglobulin isotypes with normal or low numbers of B cells
|
|
| CIM11 |
4A01.02 |
Specific antibody deficiency with normal immunoglobulin concentrations or normal number of B cells
|
|
| CIM11 |
4A01.03 |
Transient hypogammaglobulinaemia of infancy
|
|
| CIM11 |
4A01.04 |
Immunodeficiencies with isotype or light chain deficiencies with normal number of B cells
|
|
| CIM11 |
4A01.05 |
Immunodeficiencies with severe reduction in serum IgG or IgA with normal or elevated IgM and normal numbers of B-cells
|
|
| CIM11 |
4A01.1 |
Combined immunodeficiencies
|
|
| CIM11 |
4A01.10 |
Severe combined immunodeficiencies
|
|
| CIM11 |
4A01.11 |
Major histocompatibility complex class I deficiency
|
|
| CIM11 |
4A01.12 |
Major histocompatibility complex class II deficiency
|
|
| CIM11 |
4A01.2 |
Diseases of immune dysregulation
|
|
| CIM11 |
4A01.20 |
Immune dysregulation syndromes with hypopigmentation
|
|
| CIM11 |
4A01.21 |
Immune dysregulation syndromes presenting primarily with autoimmunity
|
|
| CIM11 |
4A01.22 |
Immune dysregulation syndromes presenting primarily with lymphoproliferation
|
|
| CIM11 |
4A01.23 |
Primary haemophagocytic lymphohistiocytosis
|
|
| CIM11 |
4A01.3 |
Other well-defined immunodeficiency syndromes due to defects in adaptive immunity
|
|
| CIM11 |
4A01.30 |
Immunodeficiency due to defects of the thymus
|
|
| CIM11 |
4A01.31 |
DNA repair defects other than combined T-cell or B-cell immunodeficiencies
|
|
| CIM11 |
4A01.32 |
Immuno-osseous dysplasia
|
|
| CIM11 |
4A01.33 |
Hepatic veno-occlusive disease - immunodeficiency syndrome
|
|
| CIM11 |
4A01.34 |
Hyperimmunoglobulin E syndromes
|
|
| CIM11 |
4A20 |
Acquired immunodeficiencies
|
|
| CIM11 |
4A20.0 |
Adult-onset immunodeficiency
|
|
| CIM11 |
4A20.1 |
Acquired immunodeficiency due to loss of immunoglobulin
|
|
| CIM11 |
4A20.2 |
Secondary haemophagocytic lymphohistiocytosis
|
|
| CIM11 |
4A20.20 |
Haemophagocytic syndrome associated with infection
|
|
| CIM11 |
4A20.21 |
Haemophagocytic lymphohistiocytosis associated with a malignant disease
|
|
| CIM11 |
4A40 |
Lupus erythematosus
|
|
| CIM11 |
4A40.0 |
Systemic lupus erythematosus
|
|
| CIM11 |
4A40.00 |
Systemic lupus erythematosus with skin involvement
|
|
| CIM11 |
4A40.1 |
Drug-induced lupus erythematosus
|
|
| CIM11 |
4A41 |
Idiopathic inflammatory myopathy
|
|
| CIM11 |
4A41.0 |
Dermatomyositis
|
|
| CIM11 |
4A41.00 |
Adult dermatomyositis
|
|
| CIM11 |
4A41.01 |
Juvenile dermatomyositis
|
|
| CIM11 |
4A41.1 |
Polymyositis
|
|
| CIM11 |
4A41.10 |
Juvenile polymyositis
|
|
| CIM11 |
4A41.11 |
Paraneoplastic polymyositis
|
|
| CIM11 |
4A41.2 |
Inclusion body myopathy
|
|
| CIM11 |
4A41.20 |
Inflammatory inclusion body myositis
|
|
| CIM11 |
4A41.21 |
Noninflammatory inclusion body myopathy
|
|
| CIM11 |
4A42 |
Systemic sclerosis
|
|
| CIM11 |
4A42.0 |
Paediatric onset systemic sclerosis
|
|
| CIM11 |
4A42.1 |
Diffuse systemic sclerosis
|
|
| CIM11 |
4A42.2 |
Limited systemic sclerosis
|
|
| CIM11 |
4A43 |
Overlap or undifferentiated nonorgan specific systemic autoimmune disease
|
|
| CIM11 |
4A43.0 |
IgG4 related disease
|
|
| CIM11 |
4A43.1 |
Mikulicz disease
|
|
| CIM11 |
4A43.2 |
Sjögren syndrome
|
|
| CIM11 |
4A43.20 |
Primary Sjögren syndrome
|
|